001437336 000__ 03887cam\a2200577\i\4500 001437336 001__ 1437336 001437336 003__ OCoLC 001437336 005__ 20230309004143.0 001437336 006__ m\\\\\o\\d\\\\\\\\ 001437336 007__ cr\un\nnnunnun 001437336 008__ 210615s2021\\\\sz\a\\\\o\\\\\001\0\eng\d 001437336 019__ $$a1257077358$$a1262379670 001437336 020__ $$a9783030701079$$q(electronic bk.) 001437336 020__ $$a3030701077$$q(electronic bk.) 001437336 020__ $$z9783030701062 001437336 020__ $$z3030701069 001437336 0247_ $$a10.1007/978-3-030-70107-9$$2doi 001437336 035__ $$aSP(OCoLC)1256541725 001437336 040__ $$aYDX$$beng$$erda$$epn$$cYDX$$dGW5XE$$dEBLCP$$dOCLCO$$dOCLCF$$dUKAHL$$dOCLCQ$$dCOM$$dOCLCO$$dCASUM$$dOCLCQ 001437336 049__ $$aISEA 001437336 050_4 $$aRC606$$b.C45 2021 001437336 08204 $$a616.97/9$$223 001437336 24500 $$aCellular primary immunodeficiencies /$$cMario Milco D'Elios, Cosima Tatiana Baldari, Francesco Annunziato, editors ; foreword by Donatella Lippi. 001437336 264_1 $$aCham :$$bSpringer,$$c[2021] 001437336 264_4 $$c©2021 001437336 300__ $$a1 online resource :$$billustrations (chiefly color) 001437336 336__ $$atext$$btxt$$2rdacontent 001437336 337__ $$acomputer$$bc$$2rdamedia 001437336 338__ $$aonline resource$$bcr$$2rdacarrier 001437336 4901_ $$aRare diseases of the immune system,$$x2282-6505 001437336 500__ $$aIncludes index. 001437336 5050_ $$a1. Primary Immunodeficiencies -- 2. Genetics of Cellular Immunodeficiencies -- 3. Phenocopies of Primary Immuno Deficiencies -- 4. Dysfunctional immune synapses in T cell immunodeficiencies -- 5. Mucosal immunity in primary immunodeficiencies -- 6. Combined Immuno Deficiencies -- 7. Congenital defects of phagocytes -- 8. Defects in intrinsic and innate immunity -- 9. Diseases of immune dysregulation -- 10. IPEX syndrome and IPEX-related disorders -- 11. Autoinflammatory disorders -- 12. Lung in Cellular Immunodeficiencies -- 13. Gut involvement in Cellular Immunodeficencies -- 14. Malignancies in Cellular Immunodeficencies -- 15. Autoimmunity in Cellular Immunodeficencies -- 16. Differential diagnostic in Cellular Immunodeficiencies -- 17. Management of Cellular Immunodeficiencies -- 18. Vaccines in Cellular Immunodeficiencies -- 19. Gene therapy in Cellular Immunodeficiencies. 001437336 506__ $$aAccess limited to authorized users. 001437336 520__ $$aThis volume of the series Rare Diseases of the Immune System presents detailed state of the art knowledge on the cellular primary immunodeficiencies; it includes extensive coverage of both basic science discoveries and the latest clinical advances in the field. The book is structured in accordance with the most recent classification of PIDs and also covers updates on the T cell immunological synapse. Readers will find comprehensive, in-depth descriptions of novel cellular PID genes and related clinical applications, mucosal T cells, and the various clinical phenotypes of cellular PIDs. Cellular Primary Immunodeficiencies will be of high value for immunologists, pediatricians, rheumatologists, oncologists, internists, and infectious disease specialists and will also be informative for MD, Master and PhD students. 001437336 588__ $$aOnline resource; title from PDF title page (SpringerLink, viewed June 21, 2021). 001437336 650_0 $$aImmunodeficiency. 001437336 650_0 $$aImmune system$$xCytopathology. 001437336 650_6 $$aImmunodéficience. 001437336 650_6 $$aSystème immunitaire$$xCytopathologie. 001437336 655_0 $$aElectronic books. 001437336 7001_ $$aD'Elios, Mario Milco,$$eeditor. 001437336 7001_ $$aBaldari, Cosima T.,$$eeditor. 001437336 7001_ $$aAnnunziato, Francesco,$$eeditor. 001437336 77608 $$iPrint version:$$tCellular primary immunodeficiencies.$$dCham : Springer, [2021]$$z3030701069$$z9783030701062$$w(OCoLC)1233167060 001437336 830_0 $$aRare diseases of the immune system.$$x2282-6505 001437336 852__ $$bebk 001437336 85640 $$3Springer Nature$$uhttps://univsouthin.idm.oclc.org/login?url=https://link.springer.com/10.1007/978-3-030-70107-9$$zOnline Access$$91397441.1 001437336 909CO $$ooai:library.usi.edu:1437336$$pGLOBAL_SET 001437336 980__ $$aBIB 001437336 980__ $$aEBOOK 001437336 982__ $$aEbook 001437336 983__ $$aOnline 001437336 994__ $$a92$$bISE