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Table of Contents
Volume 1: The Text
Abdominal Pain, Cutaneous Manifestations
Abscess (Sterile and Non-Sterile)
Acanthosis Nigricans-Like Lesions
Acidosis and Rash in the Newborn
Acneiform Eruptions
Acral Cyanosis
Acral Erythema
Acral Erythema and Scale With or Without Linear Cutoff
Acral Papules and Nodules; Knuckle Papules; Papules, Digital
Acrochordons (Skin Tags)
Acromegalic Features
Acro-osteolysis
Adrenal Disease, Cutaneous Manifestations
Ainhum
Alopecia
Alopecia and Structural Abnormalities of the Nose and Hands
Alopecia, Eyebrows
Alopecia in Neonates, Infants, and Toddlers
Alveolar Hemorrhage
Angioedema
Angiokeratoma Corporis Diffusum
Annular Lesions of Penis with Surface Changes
Annular Lesions with Surface Changes
Annular Lesions Without Surface Changes
Annular Scars
Aortic Disease in the Young
Aphthous Stomatitis
Arthritis and Rash (Polyarthritis and Monoarthritis)
Aseptic Meningitis, Cutaneous Manifestations
Atrichia and Nail Abnormalities
Atrophic Glossitis
Atrophic Lesions
Autoinflammatory Diseases
Bariatric Surgery, Cutaneous Signs of Nutrient Deficiency
Basal Cell Carcinoma Syndromes
Bioweapons
Black Dermatologic Entities
Black Oral Lesions
Blaschko-esque Entities
Blindness, Cutaneous Manifestations
Blue Lunulae
Blue Sclerae
Blue Spots
Blueberry Muffin Lesions, Neonate
Breast Asymmetry
Breast Cancer, Cutaneous Manifestations
Breast Hypertrophy (Gynecomastia) and Breast Masses
Breast Lesions
Buffalo Hump (Cervicodorsal Lipodystrophy)
Bullae and/or Vesicles
Bullae, Hemorrhagic Bullae, Hemorrhagic, Septic
Bullae in the Neonate
Bullae in Infants and Children
Bullae of the Fingers or Toes
Bullae, Transient, in Infants
Burning Tongue
Butterfly Rash
Café Au Lait Macules (CALMs), Associations
Cardiac and/or Cardiovascular Disease and Skin Lesions
CDKN2a with p14 LOSS
Cellulitis in the Immunocompromised Host
Cellulitis, Infections in the Immunocompetent Host
Cellulitis (Pseudocellulitis), Non-infectious Etiologies
Cerebriform Lesions
Chalky Material Extruded From Lesions
Cheilitis (Crusted Lips)
Chemotherapy, Cutaneous Manifestations
Chest Wall Tumors
Cleft Lip and/or Palate (Associated Skin Disorders)
Coarse Facies and Coarse Facial Skin
Cobblestone Appearance of Skin
Cobblestone Appearance of the Oral Mucosa
Cocaine Use, Cutaneous Manifestations
Concentric Lesions
Conjunctival Lesions, Pigmented
Craniosynostosis
Cutaneous Horns
Cutis Laxa-like Appearance
Cutis Verticis Gyrata
Cysts With or Without Drainage
Deafness or Hearing Impairment, Cutaneous Manifestations
Dermatitis (Spongiotic), Differential Diagnosis
Dermatitis, Facial, Pediatric
Dermatitis, Periorbital
Dermatitis, Periorificial
Dermatographism
Desmoplakin Mutations
Diabetes Mellitus, Cutaneous Manifestations
Diarrhea, Cutaneous Manifestations
Dimples
Doughy Skin
Drug Abuse, Cutaneous Manifestations
Dyschromatosis (Hypopigmentation and Hyperpigmentation)
Dyshidrosis
Ear Lesions
Ear, Hard (Petrified Auricles)
Ears, Red
Edema
Edema, Hands
Edema, Head
Edema, Legs
Erosions (Superficial Ulcers)
Erythroderma (Exfoliative Erythroderma)
Erythrodermic Infant
Eschars
Esophageal and Cutaneous Disease
Exanthem
Exfoliation (Desquamation)
Eyelid Lesions
Eyes, Red and Rash
Facial Asymmetry
Facial Dermatitis, Scaly
Facial Edema
Facial Papules and Plaques
Facial Papules
Facial Plaques, Scarring and Non-scarring
Facial Scars
Facial Ulcers
Facies
Fetal Akinesia Deformation Sequence
Fever and Rash, Noninfectious
Fever, Arthritis, and Exanthem
Fibromatoses in Children
Fibrous Tumors, Differential Diagnosis
Figurate Erythemas
Fingertip Lesions
Fingertip Necrosis
Fingertip Ulcers
Flushing Disorders
Follicular Plugging
Foot Ulcers
Freckling of Hands
Gastrointestinal Cancer and Skin Lesions
Gastrointestinal Hemorrhage and Skin Lesions
Gastrointestinal Polyposis and Skin
Gingival Hyperplasia
Gingivitis
Glomerulonephritis, Cutaneous Manifestations
Granulomas
Granulomatosis With Polyangiitis, Cutaneous Manifestations
Green Pigmentation
Hair Abnormalities
Hair Breakage
Hair Shaft Nodules or Nits (Particulate Matter)
Hair, Premature Graying
Heart Block and Rash
Heart Failure, Cutaneous Manifestations
Heliotrope
Hematologic Malignancies, Cutaneous Signs
Hemihypertrophy (Asymmetric Overgrowth Syndromes) Herpetiform Lesions
Heterochromia Iridum (Iridis)
Hoarseness, Cutaneous Manifestations
Human Papilloma Virus-Associated Immunodeficiency Syndromes
Hyperhidrosis
Hyperkeratotic Lesions
Hyperkeratotic Lesions of Feet
Hyperkeratotic Lesions of Hands
Hyperkeratotic Lesions of the Nipples
Hyperpigmentation in Blaschko's Lines
Hyperpigmentation, Diffuse
Hyperpigmentation, Facial
Hyperpigmentation, Flagellate
Hyperpigmentation, Paronychial
Hyperpigmentation, Patchy
Hyperpigmentation, Segmental or Zosteriform
Hyperpigmented Lesions, Discrete Annular
Hypertrichosis, Generalized
Hypertrichosis, Localized
Hypohidrosis (Anhidrosis)
Hypopigmented Patches or Plaques
Hypoplasia of Distal Phalanges
Hypotrichosis With Growth and Mental Retardation
Ichthyosiform Eruptions
Immune Deficiency Syndromes with Bacterial Infections
Inguinal Lymphadenitis and Rash
Intertrigo, Including Diaper Dermatitis
Iris Lesions, Pigmented
Islands of Sparing
Kaposi's Sarcoma, Differential Diagnosis
Kinky Hair
Knuckle Papules
Knuckles, Pebbly, With Scarring
Lacrimal Gland, Enlarged
Lentigines
Leonine Facies
Leukoderma, Guttate
Leukonychia
Leukoplakia
Linear Erythronychia
Linear Hypopigmentation
Linear Lesions
Linear Lesions Following Veins
Lip Lesions, Pigmented
Lip Papules
Lip Pits
Lips, Swollen
Lipoma Syndromes
Lithium, Cutaneous Side Effects
Livedo Reticularis With or Without Necrosis
Liver Disease, Cutaneous Manifestations and Hepatic Abnormalities of Skin Disease
Lymphadenopathy for the Dermatologist
Macrocephaly
Macrodactyly (Enlarged Digit)
Malodorous Skin Conditions
Marfanoid Features
Masses of the Head and Neck
Melanoma, Clinical Simulators
Melanonychia
Microcephaly
Micronychia and Anonychia
Midline Facial Nodules of Children
Midline Nasal Masses
Milia or Milia-Like Lesions (Fine White Papules)
Monoclonal Gammopathy, Cutaneous Manifestations
Mucinoses
Mucocutaneous Candidiasis Syndromes
Muscle Weakness and Rash
Myocarditis, Cutaneous Manifestations
Nail Abnormalities
Nasal Infiltration or Enlargement
Nasal Septal Ulceration/Perforations (Rhinophagic Ulceration)
Neck Lesions
Neck Papules
Necrosis
Neural Tube Dysraphism
Nevi, Associated Syndromes
Nipple Dermatitis
Nipple Lesions
No Fingerprint Syndromes (Adermatoglyphia, Absent Dermatoglyphics)
Nodules, Congenital
Nodules, Foot
Nodules, Juxta-Articular
Nodules, Knee
Nodules, Multilobulated
Nodules, Multiple, Subcutaneous
Nodule, Red, Face
Nodule, Red, Hand
Nodule, Red, Extremities
Nodules, Red or Violaceous, Vascular Appearance
Nodules, Skin Colored
Nodules, Ulcerated
Nodules, Unspecified Location
Normal Skin (Barely Perceptible Lesions)
Obesity Syndromes/Protuberant Abdomen
Onycholysis
Oral Mucosa, Blue Pigmentation
Oral Mucosa, Cysts
Oral Mucosa, Hyperpigmentation
Oral Mucosa, Nodules
Oral Mucosa, Ulceration
Oral Mucosa, Verrucous and Vegetating Lesions
Osteoma Cutis
Overgrowth Syndromes
P63-Associated Disorders
Painful Tumors
Palatal Necrosis (Necrotic Ulcers of the Palate)
Palmar and/or Plantar Erythema
Palmar and/or Plantar Nodules
Palmar Pits and Punctate Keratoses/Dyshidrosis-like Lesions
Palmoplantar Keratodermas
Palmoplantar Keratodermas With Atrichia or Hypotrichosis
Papules, Crusted
Papules, Digital
Papules, Dirty Brown
Papules, Distal Digital, White
Papules, Facial, Solitary
Papules, Flat-Topped
Papules, Follicular (Folliculocentric, Including Folliculitis)
Papules, Hyperkeratotic
Papules and Nodules, Hyperpigmented (With or Without Hyperkeratosis)
Papules,

Hyperpigmented With Hypertrichosis
Papules of the Nose
Papules, Periorbital
Papules, Red
Papules, Skin Colored
Papules, Unspecified
Papulosquamous Eruptions
Paraneoplastic Dermatoses
Paraproteinemias, Cutaneous Manifestations
Parathyroid Disease, Cutaneous Manifestations
Paronychia
Parotid Gland Enlargement
Particulate Matter/Exfoliation
Pedunculated (Polypoid) Lesions
Penile Edema, Acute and Chronic
Penile Lesions
Penile Ulcers
Perianal Dermatitis and Hypertrophic Plaques
Perianal Ulcers, Single or Multiple
Periorbital Edema/Erythema (Dermatitis)
Periorbital Facial Nodules, Pediatric
Periostitis
Peripheral Eosinophilia
Peripheral Neuropathy, Cutaneous Manifestations
Phakomatoses
Pharyngitis
Photoeruption and Seborrheic Dermatitis-Like Eruption
Pigmentary Retinopathy or Cone-Rod Dystrophy with Dermatologic Manifestations
Pituitary Disease, Cutaneous Manifestations
Pityriasis Rosea-Like Eruptions
Plantar Erythema
Pneumonia and Pneumonia-associated Disease, Cutaneous Manifestations
Poikilodermas of Adulthood
Poikilodermas of Childhood
Poliosis, Localized or Generalized (Canites)
Polydactyly (PPD, PAP, and Complex Types)
Pore
Port Wine Stain
Preauricular Sinuses (Ear Pits)
Pregnancy, Cutaneous Manifestations
Premature Aging Syndromes (Progeroid Syndromes)
Primary Immunodeficiency and Granuloma Formation
Proptosis
Pruritic Tumors
Pruritus, Anal
P.

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