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Foreword; References; Contents; 1: Musculoskeletal Manifestations of Hemophilia; 1.1 Introduction; 1.2 Management of Muscle Hematomas and Their Complications; 1.2.1 Compartment Syndrome and Compression Neuropathy; 1.2.2 Hemophilic Pseudotumors; 1.3 Management of Hemophilic Arthropathy; 1.3.1 Hemarthrosis; 1.3.2 Synovitis; 1.3.3 Advanced Joint Disease; 1.4 Potential Complications of Treatment; Conclusions; References; 2: Hematological Concepts and Hematological Perioperative Treatment; 2.1 Introduction; 2.2 Replacement Therapy for Orthopedic Procedures in Hemophilia

2.2.1 Optimal Level and Duration of Replacement Therapy2.2.2 Bolus Infusion (BI) and Continuous Infusion (CI) of Factor Concentrates; 2.3 Orthopedic Surgery in Hemophilia Patients with Inhibitors; Conclusions; References; 3: Hemophilic Hemarthroses: Diagnosis and Management; 3.1 Introduction; 3.2 Acute Hemarthroses; 3.2.1 Hematological Treatment; 3.2.2 Rest and Splinting; 3.2.3 Ice; 3.2.4 Analgesia; 3.2.5 Joint Aspiration (Arthrocentesis); 3.2.6 Arterial Embolization; 3.3 Recurrent Hemarthroses; Conclusions; References; 4: Imaging of the Hemophilic Joints; 4.1 Introduction; 4.2 Radiography

4.3 Ultrasonography4.4 Magnetic Resonance Imaging; 4.5 Other Imaging Techniques; 4.5.1 Computed Tomography (CT); 4.5.2 Nuclear Medicine; 4.5.3 Positron Emission Tomography (PET); Conclusions; References; 5: Shoulder Surgery in Hemophilia; 5.1 Introduction; 5.2 Clinical Findings; 5.3 Radiological Findings; 5.4 Management; 5.4.1 Acute Hemarthrosis; 5.4.2 Synovectomy; Medical Synovectomy (Synoviorthesis); Arthroscopic Synovectomy; Open Synovectomy; 5.4.3 Shoulder Replacement; 5.4.4 Arthrodesis; Conclusions; References; 6: Surgery of the Elbow in Hemophilia; 6.1 Introduction; 6.2 Epidemiology

6.3 Clinical Findings6.4 Radiological Findings; 6.5 Management; 6.5.1 Conservative Management; 6.5.2 Synovectomy; Indication for Synovectomy; Open Surgical Synovectomy; Arthroscopic Synovectomy; Results of Synovectomy; 6.5.3 Total Elbow Arthroplasty; Total Elbow Arthroplasty; Surgical Technique; Results of Elbow Arthroplasty; Conclusions; References; 7: Hip Surgery in Hemophilia; 7.1 Introduction; 7.2 Management of Hip Hemophilic Arthropathy; 7.3 Muscular Disorders of the Hip in the Hemophilic Patient; Conclusions; References; 8: Knee Surgery in Hemophilia; 8.1 Introduction

8.2 General Concepts8.3 Articular Puncture (Drainage of Hemarthrosis); 8.4 Synovectomy; 8.5 Handling Knee Flexion Contractures; 8.6 Articular Arthroscopic Debridement; 8.7 Alignment Osteotomy; 8.8 Total Knee Replacement (TKR); Conclusions; References; 9: Advanced Hemophilic Arthropathy of the Ankle: Total Ankle Replacement or Ankle Fusion?; 9.1 Introduction; 9.2 Search Strategy; 9.3 Results of TAR and Arthrodesis; 9.4 Comparative Studies: TAR vs Arthrodesis; 9.5 Total Ankle Replacement (TAR) or Arthrodesis of the Ankle in Hemophilia; 9.6 Author's Experience; Conclusions; References

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