Preface; Contents; Contributors; Part I: Introduction, Epidemiology and Pathology; 1: Overview of Type 1 and Type 2 AIP; Introduction; The First Report of AIP; Type 1 AIP; Clinical Features; Laboratory Features; Imaging Features; Histopathological Features; Diagnostic Criteria and Differential Diagnosis; Treatment; Prognosis; Type 2 AIP; Conclusions; References; 2: Epidemiology of Autoimmune Pancreatitis; Introduction; First Nationwide Survey of AIP in Japan; Second Nationwide Survey in Japan; Diagnosis; Treatment; Relapse; Third Nationwide Survey in Japan

International AIP Surveys Summary; References; 3: Pathophysiology of Autoimmune Pancreatitis; Introduction; Immunogenic Backgrounds; Innate Immunity; Possible Roles of IgG4 in Type 1 AIP; The Complement System; Autoantibodies and Candidate of Target Antigens; Role of B Cells; Th1 and Th2 Immune Balance; Regulatory T Cells; Hypothesis for the Pathogenesis of Type 1 AIP; Conclusion; References; 4: Pathology; General Considerations; Type 1 AIP/LPSP; Storiform Fibrosis; Pancreatic Parenchymal Inflammation; Ductal Inflammation; Lobular Inflammation; Nonparenchymal Tissue Inflammation

Peripancreatic InflammationVascular Inflammation; Nervous Inflammation; IgG4 Immunostaining; Histological Diagnostic Criteria of Type 1 AIP; Special Conditions That Could Be Associated with Type 1 AIP; Type 2 AIP/IDCP; Ductal Inflammation; Lobular Inflammation; Histological Diagnostic Criteria of Type 2 AIP; Biopsy Diagnosis of AIP; Concluding Remarks; References; 5: Pancreatic Endocrine and Exocrine Functions in Patients with Autoimmune Pancreatitis; Introduction; Endocrine Dysfunction Associated with Type 1 AIP; Exocrine Dysfunction Associated with Type 1 AIP

Pancreatic Exocrine and Endocrine Functions After Steroid Therapy in AIPThe Management of Pancreatic Exocrine Insufficiency in Patients with AIP Associated with Pancreatic Diabetes; Conclusion; References; 6: Type 2 AIP; Introduction; Epidemiology of Type 2 AIP; Imaging Features of Type 2 AIP; Histopathology of Type 2 AIP; Clinical Manifestations of Type 2 AIP; Diagnosis of Type 2 AIP; Treatment and Follow-Up; Conclusion; References; Part II: Diagnosis; 7: Diagnostic Criteria of Autoimmune Pancreatitis; Introduction; The JPS Diagnostic Criteria 2002 and 2006

Diagnostic Criteria in South Korea, the USA, and Europe Establishment of the International Consensus Criteria; Overview of the ICDC; Type 1 AIP; Type 2 AIP; AIP-Not Otherwise Specified (NOS); ICDC and the JPS Diagnostic Criteria 2011; Comparison of the Different Diagnostic Criteria for AIP; Differential Diagnosis Between AIP and Pancreatic Cancer; Summary; References; 8: Clinical Features; Introduction; Clinical Features; Distinguish AIP from Malignancy; Natural History and Prognosis of AIP; Summary; References; 9: Serology; Introduction; Diagnosis; Marker Sensitivities