Unlimited

Authorized users

Can lend chapters, not whole ebooks

Treatment of cystic fibrosis and other rare lung diseases / Arata Azuma, Michael S. Schechter, editors.

9783034809771 (electronic book)
3034809778 (electronic book)
9783034809757

Switzerland : Springer, 2017.

English

1 online resource.

10.1007/978-3-0348-0977-1 doi

RC858.C95

616.3/72

This volume describes the pathogenesis and pathophysiology of several pulmonary diseases as well as their treatment. It also discusses the underlying genetic and molecular biological basis, which opens the way for new treatments for these conditions. It focuses on the treatment of cystic fibrosis including CFTR (cystic fibrosis transmembrane-conductance regulator) modulator therapies, drug therapies that augment airway surface liquid as well as anti-inflammatory and anti-infective therapies. Further topics include long-term, low-dose macrolide therapy for diffuse panbronchiolitis; novel agents for previously untreatable idiopathic pulmonary fibrosis; possible new treatments for pulmonary alveolar proteinosis (PAP); and multiple novel therapeutic targets for treating lymphangiomyomatosis. Research into these conditions has led to major advances in our understanding of the underlying genetic and molecular basis of this disease, and to dramatic improvements in survival and quality of life for affected individuals.

Includes bibliographical references.

Access limited to authorized users.

text file PDF

Online resource; title from PDF title page (SpringerLink, viewed February 9, 2017).

Milestones in drug therapy.

Print version: 9783034809757

Online Resources > Ebooks
All Resources